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Noninvasive ventilation for paediatric patients

Children with inherited neuromuscular conditions such as spinal muscular atrophy (SMA), Duchenne’s muscular dystrophy (DMD), Ullrich congenital muscular dystrophy and X-linked myotubular myopathies are at high risk of respiratory disorders during early childhood or adolescence.1

The British Thoracic Society guidelines for respiratory management of children with neuromuscular weakness recommends annual sleep studies for patients who have symptoms of sleep apnoea or nocturnal hypoventilation (shallow breathing).2 Children with rigid spine syndrome and diaphragmatic weakness should be closely monitored for symptoms and may need more frequent sleep studies.1,3

Noninvasive ventilation is recommended in patients with daytime hypercapnia (elevated levels of carbon dioxide) and symptomatic nocturnal hypoventilation. NIV use has been shown to:

  • Improve pulmonary gas exchange and manage chronic hypoventilation4,5
  • Improve health related quality of life4,5
  • Improve sleep related symptoms5
  • Reduce hospital readmissions for acute ventilatory decompensation1,5
  • Increase survival in neuroMND, type I SMA, ALS and DMD patients6,7,8,9

To ensure optimal outcomes, doctors should closely monitor the efficacy of NIV and patient adherence to therapy.1


Find out more about noninvasive ventilation on our dedicated ResMed page

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