ResMed Logo

Noninvasive ventilation for paediatric patients

Children with inherited neuromuscular conditions such as spinal muscular atrophy (SMA), Duchenne’s muscular dystrophy (DMD), Ullrich congenital muscular dystrophy and X-linked myotubular myopathies are at high risk of respiratory disorders during early childhood or adolescence.1

The British Thoracic Society guidelines for respiratory management of children with neuromuscular weakness recommends annual sleep studies for patients who have symptoms of sleep apnoea or nocturnal hypoventilation (shallow breathing).2 Children with rigid spine syndrome and diaphragmatic weakness should be closely monitored for symptoms and may need more frequent sleep studies.1,3

Noninvasive ventilation is recommended in patients with daytime hypercapnia (elevated levels of carbon dioxide) and symptomatic nocturnal hypoventilation. NIV use has been shown to:

  • Improve pulmonary gas exchange and manage chronic hypoventilation4,5
  • Improve health related quality of life4,5
  • Improve sleep related symptoms5
  • Reduce hospital readmissions for acute ventilatory decompensation1,5
  • Increase survival in neuroMND, type I SMA, ALS and DMD patients6,7,8,9

To ensure optimal outcomes, doctors should closely monitor the efficacy of NIV and patient adherence to therapy.1

Find out more about noninvasive ventilation on our dedicated ResMed page

More Articles

Noninvasive ventilation for acute respiratory failure
Non-invasive ventilation (NIV) is often used for patients with Chronic Obstructive Pulmonary Disease, but emerging evidence suggests that NIV can be used in treating other types of acute respiratory failure.
Noninvasive ventilation for COPD patients
Treatment of COPD with noninvasive ventilation (NIV) has been shown to be effective in treating acute exacerbations of COPD, assisting pulmonary rehabilitation in COPD patients, and providing benefits in managing chronic hypercapnic COPD patients.
Noninvasive ventilation for neuromusclar diseases in adults
Many chronic neuromuscular disorders lead to progressive respiratory muscle dysfunction. Non-invasive ventilation can help reduce daytime sleepiness while facilitating gas exchange and breathing.